|
Hemophilia Factors
- Individuals
with bleeding disorders do not bleed faster. They bleed
LONGER due to their body’s inability to clot adequately.
- Affects
all socioeconomic and racial groups equally
- Severity
level is consistent between family members
- Bleeding
episodes can occur spontaneously or after some kind of trauma.
The History
 Earliest
records documenting this disorder date back 2,300 years. Known
as the “Royal Disease”. Queen Victoria of England
was an obligatory carrier of the defective gene, consequently
passing the gene to the royal houses of Spain, Germany and
Russia.
- In the 1800’s, blood transfusions were given to persons
that had hemophilia to control their bleeding.
- In the 1960’s, cryoprecipitate was discovered and was
used for the treatment of hemophilia.
- In the 1970’s, development of factor VIII and factor
IX concentrates were used for the treatment of hemophilia.
- In the 1980’s, HIV and HEPATITIS were discovered in the
blood supply and many community members lost their lives as
result of infection.
|
|
In the 1990’s, manufacturers developed and introduced
to the community plasma-free concentrates (recombinant)
because safety was the number one concern.
Today, children living with hemophilia live long, active,
healthy lives thanks to the advances in medicine
|
Hemophilia is...
A rare genetic bleeding disorder caused by the absence or
deficiency of one of the blood clotting proteins manufactured
in the liver and found in the blood.
The most common types of hemophilia are:
- Factor VIII (hemophilia A) deficiency
- Factor IX (hemophilia B) deficiency
Hemophilia is classified as mild, moderate, or severe depending
on the amount of clotting factor VIII or IX in the blood.
| Normal |
50-150% is normal |
| Mild hemophilia |
6-49% |
| Moderate hemophilia |
1-5% |
| Severe hemophilia |
<1% |
Left untreated, hemophilia often leads to severe joint damage,
permanent disabilities and premature death.
Hemophilia affects around 20,000 persons in the United States.
Almost exclusively male
Factor VIII, hemophilia A = 80%
Factor IX, hemophilia B = 20%
70% of the hemophilia population is affected by the severe
level.
Hemophilia occurs in 1 out of 7,500 male births
50% of individuals affect are under the age of 20 years
Are You Having
A Bleed?
Complaints of tingling, bubbling, pain, stiffness or decreased
motion in any limb or appears to have a part of the body (usually
a joint) that is swollen or warm to the touch or appears to
favor an arm or leg more than usual or limps or refuses to
use a limb.
Serious Bleeds are considered:
Intra-cranial
Spinal Cord
Throat
Intra-abdominal
Limb compartments (calf, forearm, psoas muscle)
Ocular
Joint Bleeds
and Muscle Bleeds
- Treat with prescribed factor concentrate
- Rest
- Ice
- Compression
- Elevation
Nose Bleeds
- Position patient sitting straight up with head upright
- Pinch the bridge of the nose using firm continuous pressure
for 20 minutes
- Apply a cold pack to the back of the neck
- Check with HTC team for medicine options
Mouth Bleeds
- Apply ice compresses with firm, continuous pressure for
20 minutes
- For Teeth- Apply a wet tea bag wrapped in gauze around
the tooth
- Check with HTC team for medicine options.
Cuts and Scrapes
- Clean the cut, scrape or laceration with an antiseptic
soap
- Apply firm pressure and elevate the body part until bleeding
stops
- Apply a sterile dressing
- Apply an ice pack to the area over the bandage or dressing
Community Support
National Hemophilia Foundation: www.hemophilia.org
Find a listing of local chapters and Hemophilia Treatment
Centers
Hemophilia Federation of America: www.hemophiliafed.org
Factor Health Management: www.factorhealth.com
|
